Surgical Management of a Giant Hypertrophic Craniofacial Low-Flow Vascular Malformation in Sturge-Weber Syndrome: A Case Report

Sturge-Weber syndrome is a rare neurocutaneous vascular disorder that may be associated with progressive hypertrophic craniofacial vascular malformations causing significant functional and aesthetic impairment. We report the case of a 53-year-old man with long-standing epilepsy who presented with a giant hypertrophic vascular malformation involving the left fronto-palpebral region, resulting in visual obstruction, recurrent maceration, malodor, and severe facial disfigurement. Doppler ultrasound demonstrated a low-flow lesion without evidence of arteriovenous shunting, while brain magnetic resonance imaging revealed characteristic intracranial findings of Sturge-Weber syndrome. Complete surgical excision followed by split-thickness skin graft reconstruction was performed. Histopathological examination confirmed a benign vascular malformation. At 4-month follow-up, stable graft coverage, marked improvement in facial contour and visual access, and resolution of local hygienic problems were achieved without recurrence or major complications.