| Nitisinone | 🇺🇸Verenigde Staten | 10MG, 20MG, 2MG … | capsule | In de handel | Eton |
| Nitisinone Dipharma | 🇮🇹Italië | | Capsula rigida | Toegelaten | Dipharma Arzneimittel GmbH |
| Nitisinone MDK 2 MG Capsulas Duras | 🇪🇸Spanje | 2 mg | cápsula dura | In de handel | Mendelikabs Europe Limited |
| Nitisinone MDK 5 MG Capsulas Duras | 🇪🇸Spanje | 5 mg | cápsula dura | In de handel | Mendelikabs Europe Limited |
| Nitisinone MDK 10 MG Capsulas Duras | 🇪🇸Spanje | 10 mg | cápsula dura | In de handel | Mendelikabs Europe Limited |
| Nitisinone Dipharma 2 mg, harde capsules | 🇳🇱Nederland | | Capsule, hard | Toegelaten | Dipharma Arzneimittel GmbH |
| Nitisinone Dipharma 5 mg, harde capsules | 🇳🇱Nederland | | Capsule, hard | Toegelaten | Dipharma Arzneimittel GmbH |
| Nitisinone Dipharma 10 mg, harde capsules | 🇳🇱Nederland | | Capsule, hard | Toegelaten | Dipharma Arzneimittel GmbH |
| Nitisinone Dipharma 20 mg, harde capsules | 🇳🇱Nederland | | Capsule, hard | Toegelaten | Dipharma Arzneimittel GmbH |
| Nitisinone LogixX Pharma | 🇳🇿Nieuw-Zeeland | | Cap 2 mg | Vergoed | |
| Nitisinone LogixX Pharma | 🇳🇿Nieuw-Zeeland | | Cap 10 mg | Vergoed | |
| Nitisinone LogixX Pharma | 🇳🇿Nieuw-Zeeland | | Cap 5 mg | Vergoed | |
| MDK-Nitisinone | 🇨🇦Canada | 2 MG | Capsule | In de handel | Mendelikabs INC |
| MDK-Nitisinone | 🇨🇦Canada | 5 MG | Capsule | In de handel | Mendelikabs INC |
| MDK-Nitisinone | 🇨🇦Canada | 10 MG | Capsule | In de handel | Mendelikabs INC |
| MDK-Nitisinone | 🇨🇦Canada | 20 MG | Capsule | Niet in de handel | Mendelikabs INC |
| Nitisinone Tablets | 🇨🇦Canada | 5 MG | Tablet | Vervallen | Cycle Pharmaceuticals LTD. |
| Nitisinone Tablets | 🇨🇦Canada | 10 MG | Tablet | Vervallen | Cycle Pharmaceuticals LTD. |
| Nitisinone Tablets | 🇨🇦Canada | 2 MG | Tablet | Vervallen | Cycle Pharmaceuticals LTD. |
| Nitisinone MDK (previously Nitisinone MendeliKABS) | 🇪🇺Europese Unie | | | Ingetrokken | MendeliKABS Europe Ltd |
| Nityr | 🇺🇸Verenigde Staten | 10MG, 2MG, 5MG | tablet | In de handel | Cycle |
| NITISINONE MENDELIKABS 2 mg | 🇷🇴Roemenië | 2 mg | caps. | Status onbekend | Mendelikabs Europe Limited |
| NITISINONE MENDELIKABS 5 mg | 🇷🇴Roemenië | 5 mg | caps. | Status onbekend | Mendelikabs Europe Limited |
| NITISINONE MENDELIKABS 10 mg | 🇷🇴Roemenië | 10 mg | caps. | Status onbekend | Mendelikabs Europe Limited |
| Harliku | 🇺🇸Verenigde Staten | 2MG | tablet | In de handel | Cycle |