An Extremely Rare Association of the Giant Right Atrium with Uncorrected Tetralogy of Fallot in an Adolescent Male Patient

ABSTRACT Uncorrected tetralogy of Fallot (TOF) can be associated with widespread abnormalities, but the giant right atrium (RA) is an extremely rare one. The giant RA can cause additional problems causing atrial arrythmias, thromboembolism, and compression of adjacent structures. Tricuspid regurgitation is common with annular dilatation. In symptomatic cases, reduction atrioplasty is recommended. Sternotomy should be careful to avoid damage to the giant RA. In asymptomatic cases, anticoagulation should be carried out. We report a rare case of uncorrected TOF associated with the giant RA and got successfully treated with surgery.